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Anales de la Facultad de Medicina
versão impressa ISSN 1025-5583
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ROMANI, Franco; CUADRA, José; ATENCIA, Fernando e CANELO, Carlos. Waldenströms macroglobulinemia: report of a case. An. Fac. med. [online]. 2008, vol.69, n.2, pp.112-116. ISSN 1025-5583.
Waldenströms macroglobulinaemia (WM) is a rare haematological neoplasm characterized by bone marrow infiltration of lymphoplasmatic lymphoma and IgM monoclonal gammopathy. We report a case of a black patient with WM that presented ocular manifestations with funduscopic findings, neurologic manifestations, cytopenia, and constitutional symptoms related to tumor infiltration and monoclonal gammopathy. Also osteolytic bone lesions, rare in MW. We review the literature on the diagnostic criteria, epidemiology, pathogenesis and clinical manifestations of this disorder, unusual in our country.
Palavras-chave : Waldenstrom macroglobulinemia; neoplasms; viscosity; paraproteinemias.