Abstract

TORRES-RAMIREZ, Luis; OSORIO-MARCATINCO, Víctor; VELEZ-ROJAS, Miriam  and  FLORES-MENDOZA, Martha. Idiopathic opsoclonus-myoclonus syndrome in an adult patient: a case report. Rev Neuropsiquiatr [online]. 2014, vol.77, n.3, pp.187-187. ISSN 0034-8597.

We report a case of 31 a year old male patient with opsoclonus-myoclonus syndrome, a rare entity which is characterized by multidirectional eye movements (opsoclonus) and myoclonus.  It can be associated with ataxia, tremor and altered level of consciousness. This entity is reported as secondary manifestation of infectious, paraneoplastic or idiopathic disease, the more common etiologies in adult population. There is evidence of an immunological mechanism involved in its pathogenesis. The treatment with steroids and/or immunomodulator drugs is widely used although there are no trials supporting its long term use in clinical improvement. Our patient received early steroid treatment with a prompt improvement and recovery. It is important to recognize this entity for the possibility of being related with underlying malignancies.

Keywords : Ocular motility disorders; myoclonus; ataxia; adult.

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