Revista Medica Herediana
versión On-line ISSN 1729-214X
DIAZ-PLASENCIA, Juan et al. Desmoid Tumors: clinical findings, treatment and survival. Rev Med Hered [online]. 1998, vol.9, n.2, pp. 69-76. ISSN 1729-214X.
Objective: To identify the clinical picture and the 5 year recurrence and survival rates. Material and methods: We analized information on 18 patients managed at Belén Hospital, Trujillo, Peru from 1966 through 1994. Results: The most frequent antecedents were recent pregnancy (n=8), previous surgery (n=3) and trauma (n=1). The mean age was 29.5 ± 16.7 years (range, 5 months to 75 years). Fifty percent of the tumours appeared on third decade of life. There were 6 men and 12 women (M:F, 1:2). The most common symptom and sign was tumour (100%) followed by pain (66.7%), functional impotence (22.2%) and paresthesias (16.7%). The mean tumoral diameter was 10.9 ± 5.6 cm. The most common localization of desmoid tumours was abdominal wall (n=12), head and neck (n=3) and inferior limbs (n=3). Fourteen patients underwent surgical treatment, and radiotherapy was administered in 2 non resected cases. Among the 10 patients with complete follow - up, there was a five - year recurrence rate of 33.3% (25% with surgical treatment, 25% and 50% after radiotherapy). The recurrence rate after radical surgery and local resection was of 16.7% and 50%, respectively. The five - year survival rate was 87.3% (83.3% with surgical treatment and 100% with radiotherapy). Conclusions: These type of tumours were more frecuently found in the abdominal wall. The wide - edge surgery is the safest choice of treatment for desmoid tumours. (Rev Med Hered 1998; 9: 69-76 ).
Palabras llave : Desmoid tumours; clinico - pathological picture; treatment,; recurrence; survival.