Abstract

ATAMARI-ANAHUI, Noé  and  SOLORZANO-GUTIERREZ, Sendy. Incontinentia pigmenti (Bloch-Sulzberger Syndrome) in a male patient: A case report. Rev Med Hered [online]. 2015, vol.26, n.4, pp.238-241. ISSN 1018-130X.

Incontinentia pigmenti is a rare X-linked dermatosis characterized by bullous lesions distributed along Blaschko´s lines. Four clinical stages are recognized: blister, verrucous or wart like lesions, hyperpigmentation and atrophic lesions. We present the case of a 30-day old male patient who presented with blisters and bullous lesions distributed along Blaschko´s lines. A skin biopsy was performed that confirmed the diagnosis. This is the first report of a male patient in Peru wth the syndrome.

Keywords : Incontinentia pigmenti; Skin Diseases; Genetic; male.

        · abstract in Spanish     · text in Spanish     · Spanish ( pdf )