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Horizonte Médico (Lima)
versión impresa ISSN 1727-558X
Resumen
GALVEZ-MARTICORENA, Brayan y CHAMBI-TORRES, Javier. Incontinentia pigmenti in Cajamarca: A case report on infant. Horiz. Med. [online]. 2015, vol.15, n.3, pp.57-60. ISSN 1727-558X.
Incontinentia pigmenti (IP) or Bloch-Sulzberger syndrome is a rare dominant X-linkeddisease characterized by skinlesions. It may be accompanied by neurological, ophthalmological and dental manifestations. We report the case of a one month and twenty six days old female patient diagnosed with this diseasewho was successfully treated. (Horiz Med 2015; 15(3): 57-60)
Palabras clave : Incontinentia pigmenti; Pigmentation Disorders; Skin Abnormalities.