Abstract

BORIA ALEGRE, Félix; RAMOS, Javier Lucas; ALVAREZ-LOPEZ, Covadonga  and  POZA CORDON, Joaquín. Herlyn-Werner-WÜnderlich syndrome with late diagnosis: a propos of a case. Rev. peru. ginecol. obstet. [online]. 2019, vol.65, n.3, pp.337-340. ISSN 2304-5132.  http://dx.doi.org/10.31403/rpgo.v66i2191.

Herlyn-Werner-Wünderlich syndrome is a rare congenital anomaly that affects the genitourinary system. It is defined by the triad of uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. It consists in a Mullerian anomaly. Most patients remain asymptomatic until the menarche, when they present dysmenorrhea, pelvic pain, and a pelvic mass is noticed due to hematocolpos. We present the case of a 32-year-old patient studied for infertility. 3D transvaginal ultrasound and hysterosalpingography showed uterus didelphys and a blind hemivagina. Speculoscopy during menses revealed a normal cervix and a little orifice on the lateral vagina where blood could be seen draining from a fistulized hemivagina. The abdominal ultrasound showed ipsilateral renal agenesis, confirming the suspected diagnosis.

Keywords : Mullerian ducts; Herlyn-Werner-Wünderlich syndrome.

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