Resumo

TORRES-CEPEDA, Duly; RONDON-TAPIA, Martha  e  REYNA-VILLASMIL, Eduardo. Proximal type epithelioid sarcoma of the vulva. Rev. peru. ginecol. obstet. [online]. 2022, vol.68, n.2, 00014.  Epub 06-Jul-2022. ISSN 2304-5132.  http://dx.doi.org/10.31403/rpgo.v68i2420.

Epithelioid sarcoma is a rare type of mesenchymal tumor. Proximal-type epithelioid sarcoma of the vulva is an extremely rare malignant tumor of the soft tissues with frequent recurrences due to its aggressive behaviour. Because its characteristics are similar to other benign lesions, this leads to diagnostic and therapeutic delays. Histologic features of this tumor include prominent epithelioid cells and the appearance of rhabdoid features with marked nuclear atypia. Due to its low incidence, there are no evidence-based diagnostic algorithms or published recommendations for treatment. The prognosis is generally poor. A case of proximal type epithelioid sarcoma of the vulva is presented.

Palavras-chave : Vulva; Epithelioid sarcoma; Vulvar neoplasms.

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