Abstract

VALDIVIA, José Luis Medina. Congenital pulmonary airway malformation (CPAM): A case report. Rev. Fac. Med. Hum. [online]. 2021, vol.21, n.1, pp.217-221. ISSN 1814-5469.  http://dx.doi.org/10.25176/rfmh.v21i1.3488.

Pulmonary malformations include different anomalies of the respiratory system, including congenital pulmonary airway malformation (CPAM), formerly known as cystic adenomatous malformation, which is a rare disease with an incidence of 1 per 8,300 to 35,000 live births. Five classification patterns have been described according to the number and size of the cyst, in addition to their histological characteristics, with type I CPAM being the most frequent, showing displacement of adjacent structures according to size, associated with brochioalveolar carcinoma, and favourable prognosis after surgical resection. We present the case of a four-year-old female patient with recurrent hospitalizations for pneumonia and bronchial obstructive syndrome. The careful anamnesis and physical examination supplemented with the chest X-ray and tomography allowed the diagnosis to be suspected. Later, the patient underwent surgery, there were no complications and the respiratory symptoms disappeared. The histopathological study confirmed the diagnosis.

Keywords : disease; congenital anomalies; cysts; pneumonia; hospitalized child (source: MeSH NLM)..

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